Cost and Availability of Dietary Treatment of Phenylketonuria (PKU)

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Publisher :
ISBN 13 :
Total Pages : 274 pages
Book Rating : 4.:/5 (319 download)

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Book Synopsis Cost and Availability of Dietary Treatment of Phenylketonuria (PKU) by : California. Primary Care and Family Health Division. Genetic Disease Branch

Download or read book Cost and Availability of Dietary Treatment of Phenylketonuria (PKU) written by California. Primary Care and Family Health Division. Genetic Disease Branch and published by . This book was released on 1997 with total page 274 pages. Available in PDF, EPUB and Kindle. Book excerpt:

Diet Management of PKU for Infants and Preschool Children

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Publisher :
ISBN 13 :
Total Pages : 38 pages
Book Rating : 4.3/5 (121 download)

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Book Synopsis Diet Management of PKU for Infants and Preschool Children by : Phyllis B. Acosta

Download or read book Diet Management of PKU for Infants and Preschool Children written by Phyllis B. Acosta and published by . This book was released on 1977 with total page 38 pages. Available in PDF, EPUB and Kindle. Book excerpt:

Ethical Issues in Health Care on the Frontiers of the Twenty-First Century

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Author :
Publisher : Springer Science & Business Media
ISBN 13 : 9781402003677
Total Pages : 352 pages
Book Rating : 4.0/5 (36 download)

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Book Synopsis Ethical Issues in Health Care on the Frontiers of the Twenty-First Century by : Stephen Wear

Download or read book Ethical Issues in Health Care on the Frontiers of the Twenty-First Century written by Stephen Wear and published by Springer Science & Business Media. This book was released on 2001-11-30 with total page 352 pages. Available in PDF, EPUB and Kindle. Book excerpt: of UB’s medical school, that UB developed its School of Arts and Sciences, and thus, assumed its place among the other institutions of higher education. Had Fillmore lived throughout UB’s first seventy years, he would probably have been elated by the success of his university, and he should have been satisfied and pleased that UB remained intrinsically bonded to its community while at the same time engrafting the values and standards important to higher education’s mission in the region. UB and its medical school have undergone many challenging transitions since 1846. Included among them were: (1) the completion of an academic campus in the far northeast comer of the City of Buffalo while leaving its medical, dental and law schools firmly situated in the core of downtown Buffalo; (2) the eventual relocation, after the second world war, of the law school to the newer campus in Amherst, and the medical and dental school to the original academic campus: and (3) the merger with the State University of New York System in 1962. Despite these significant transitions, any one of which could have changed the intrinsic integrity of UB and disrupted the bonding between community and university, that did not happen. To this day, the ties between community and academe persist. Fillmore and White should celebrate their success and important contribution to Buffalo and Western New York.

Living with PKU

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Publisher :
ISBN 13 : 9781739635619
Total Pages : 0 pages
Book Rating : 4.6/5 (356 download)

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Book Synopsis Living with PKU by : Pauline O'Connor

Download or read book Living with PKU written by Pauline O'Connor and published by . This book was released on 2022-06-18 with total page 0 pages. Available in PDF, EPUB and Kindle. Book excerpt: Living with PKU: A low protein life with Phenylketonuria is a new and valuable resource for adults and teens with Phenylketonuria (PKU), or for families new to the disorder. Pauline has lived with PKU for over forty years. In this honest account, she shares her experience and mistakes to help others navigating the difficult dietary treatment. In clear and simple language, this book explains PKU and offers practical advice on living with it, including: PKU and mental health Managing PKU clinics Travel & emigrating Women & PKU Healthy eating and exercise

Diet Management of PKU for Infants and Preschool Children

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Publisher :
ISBN 13 :
Total Pages : 30 pages
Book Rating : 4.:/5 (125 download)

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Book Synopsis Diet Management of PKU for Infants and Preschool Children by :

Download or read book Diet Management of PKU for Infants and Preschool Children written by and published by . This book was released on 1978 with total page 30 pages. Available in PDF, EPUB and Kindle. Book excerpt:

Public Health Reports

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Publisher :
ISBN 13 :
Total Pages : 436 pages
Book Rating : 4.:/5 (319 download)

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Book Synopsis Public Health Reports by :

Download or read book Public Health Reports written by and published by . This book was released on 1993 with total page 436 pages. Available in PDF, EPUB and Kindle. Book excerpt:

Low Protein Cookery for Phenylketonuria

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Publisher : Univ of Wisconsin Press
ISBN 13 : 9780299153847
Total Pages : 576 pages
Book Rating : 4.1/5 (538 download)

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Book Synopsis Low Protein Cookery for Phenylketonuria by : Virginia E. Schuett

Download or read book Low Protein Cookery for Phenylketonuria written by Virginia E. Schuett and published by Univ of Wisconsin Press. This book was released on 1997 with total page 576 pages. Available in PDF, EPUB and Kindle. Book excerpt: Much more than a cookbook, Low Protein Cookery for Phenylketonuria (PKU) is a practical and easy-to-use guide for those who must maintain a protein-restricted diet for treatment of PKU or similar inherited diseases of protein metabolism. It contains hundreds of helpful suggestions for managing the diet. This third edition of Low Protein Cookery for PKU appears exactly twenty years after the original 1977 publication and includes the 450-plus recipes and the hints from the 1988 second edition that have been used and enjoyed by families for nearly a decade. The major new feature of the third edition is entirely new nutrient calculations. The available food supply has changed significantly in the past fifteen years, and nutrient information is much better now. The nutrient calculations in this edition of the cookbook are based on the updated 1995 Low Protein Food List for PKU compiled by the author, which is the most widely used food list for the PKU diet in the United States. Some of the changes in nutrient values are subtle, others more significant; all reflect the best information currently available. Low Protein Cookery for PKU offers recipes that appeal to a wide range of ages, suit a wide range of individual diet requirements, and facilitate integration of the diet into normal family eating routines. Many of the recipes are suitable for the entire family; others include instructions for adapting the recipe to suit the needs of family members not on the diet, or are accompanied by recipes for the preparation of similar non-diet items. The recipes provide gram weights when appropriate, for greater accuracy in preparing the recipes and in maintaining the diet.

Low Protein Food List for PKU

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Publisher : Createspace Independent Publishing Platform
ISBN 13 : 9781456318420
Total Pages : 0 pages
Book Rating : 4.3/5 (184 download)

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Book Synopsis Low Protein Food List for PKU by : Virginia E. Schuett

Download or read book Low Protein Food List for PKU written by Virginia E. Schuett and published by Createspace Independent Publishing Platform. This book was released on 2010-12 with total page 0 pages. Available in PDF, EPUB and Kindle. Book excerpt: This book has been replaced by the online service HowMuchPhe.org, and smaller, pocket books are available at howmuchphe.org/books. The Low Protein Food List for PKU has been an indispensible resource for everyone involved in the treatment of phenylketonuria (PKU) since 1995. This third edition contains over 6,000 entries, the most extensive listing yet of foods that are potentially suitable for the diet, nearly double the number found in the previous edition. It includes many new foods found at health-oriented grocery stores, expanding choices for the diet. The book provides information on phenylalanine (phe), protein, and calorie content of foods based on serving portions, both in common measures and gram weights, in an easily searchable format. The handy "mg phe/gm food" column allows users to compare phenylalanine density of foods and make appropriate food choices for individual diet needs. People using an "exchange" system for counting phe will find exchanges are calculated for each food portion as well. The front section of the book also contains valuable information and tips for managing the PKU diet.

DHHS Publication

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Publisher :
ISBN 13 :
Total Pages : 200 pages
Book Rating : 4.:/5 (319 download)

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Book Synopsis DHHS Publication by :

Download or read book DHHS Publication written by and published by . This book was released on 1980 with total page 200 pages. Available in PDF, EPUB and Kindle. Book excerpt:

Adjuvant Treatment for Phenylketonuria: Future Research Needs

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Publisher : Createspace Independent Pub
ISBN 13 : 9781489521514
Total Pages : 104 pages
Book Rating : 4.5/5 (215 download)

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Book Synopsis Adjuvant Treatment for Phenylketonuria: Future Research Needs by : U. S. Department of Health and Human Services

Download or read book Adjuvant Treatment for Phenylketonuria: Future Research Needs written by U. S. Department of Health and Human Services and published by Createspace Independent Pub. This book was released on 2013-05-20 with total page 104 pages. Available in PDF, EPUB and Kindle. Book excerpt: Phenylketonuria (PKU) is a metabolic disorder in which an inability to properly metabolize the amino acid phenylalanine (Phe) leads to a buildup of Phe in the blood, causing neurotoxicity and resulting in intellectual disability, delayed speech, seizures and behavior abnormalities. PKU is typically diagnosed at birth following abnormal newborn screening results. With adherence to a Phe-restricted diet, poor outcomes can be mitigated. Nonetheless, management of PKU can be difficult and onerous for the patient and the family, leading to interest in identifying new ways of managing this lifelong condition. The mainstay for treatment of PKU is a diet that restricts the intake of Phe to control the Phe concentration in the blood. In 2007 the United States Food and Drug Administration approved sapropterin dihydrochloride (Kuvan®, formerly known as Phenoptin) for the treatment of PKU under the stipulation that studies regarding the drug's efficacy and long-term safety continue. Sapropterin dihydrochloride (hereafter, BH4) is presumed to work by enhancing residual enzyme activity present in some individuals with PKU. In addition to a Phe-restricted diet and BH4, another potential treatment for PKU is large neutral amino acids (LNAAs). In theory, LNAAs decrease the brain Phe concentration by competing with Phe for shared amino acid transporters to cross the blood-brain barrier. The Vanderbilt Evidence-based Practice Center completed an Agency for Healthcare Research and Quality (AHRQ)-funded systematic review of adjuvant treatments (BH4, LNAAs) for PKU. The report focused on Key Questions related to outcomes and harms of adjuvant treatment with BH4 and LNAAs in individuals with PKU, including pregnant women with PKU, and effects in subgroups (defined by demographic, clinical, genotypic, and adherence-related variables such as age, disease severity, genetic mutations, and dietary status). Key Questions also addressed evidence for optimal Phe levels for minimizing cognitive impairment. Overall, evidence was graded as insufficient to moderate to address treatment-related questions. Dietary management remains the mainstay of treatment for PKU, and maintaining control over the lifetime is an appropriate goal. Nonetheless, there is potential to support patients in achieving their clinical goals and possibly liberalizing their diet with adjuvant therapy. BH4 has been shown in two RCTs and two open label trials to reduce Phe levels in some patients, with significantly greater reductions seen in treated versus placebo groups. Overall, harms associated with the drug were minor. To date, there are no data to directly establish the potential effects of BH4 on longer term clinically important outcomes, including cognition, executive function, and quality of life. Thus, while the strength of evidence is moderate for a large, positive effect of BH4 on reducing Phe levels over the short term in some groups of patients showing initial responsiveness, evidence for the effect of BH4 on longer term clinical outcomes is low, and based on indirect associations, including a meta-analysis of the relationship of Phe levels and IQ. In theory, supplementation of a Phe-restricted diet with LNAAs might have a beneficial effect on cognition as LNAAs may competitively inhibit transportation of Phe through the bloodbrain barrier, thereby offering protection by potentially decreasing brain Phe levels. However, there was insufficient evidence to suggest that LNAAs could be a viable treatment option for reducing Phe levels or increasing Phe tolerance. Increasing Phe is clearly associated with decreased IQ, with a probability of IQ less than 85 exceeding the population probability (approximately 15 percent) at blood Phe over 400 µmol/L and leveling off at about 80 percent at 2000 µmol/L (moderate strength of evidence). This finding supports the typical target goal for blood Phe levels in individuals with PKU (120 to 360 µmol/L).

Low Protein Cookery for Phenylketonuria

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Publisher :
ISBN 13 : 9780299111403
Total Pages : 569 pages
Book Rating : 4.1/5 (114 download)

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Book Synopsis Low Protein Cookery for Phenylketonuria by : Virginia E. Schuett

Download or read book Low Protein Cookery for Phenylketonuria written by Virginia E. Schuett and published by . This book was released on 1988 with total page 569 pages. Available in PDF, EPUB and Kindle. Book excerpt: Much more than a cookbook, Low Protein Cookery for PKU (Phenylketonuria) is a practical and easy-to-use guide for those who must maintain a protein-restricted diet for treatment of PKU or similar inherited diseases of protein metabolism. It contains hundreds of helpful suggestions for managing the diet. This third edition of Low Protein Cookery for PKU appears exactly twenty years alter the original 1977 publication and includes the 450-plus recipes and the hints from the 1988 second edition that have been used and enjoyed by families for nearly a decade. The major new feature of the third edition is entirely new nutrient calculations. The available food supply has changed significantly in the past fifteen years, and nutrient information is much better now. The nutrient calculations in this edition of the cookbook are based on the updated 1995 Low Protein Food List for PKU compiled by the author, which is the most widely used food list for the PKU diet in the United States. Some of the changes in nutrient values are subtle, others more significant; all reflect the best information currently available.

Advances in Inborn Errors Amino Acid Metabolism Research and Treatment: 2011 Edition

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Publisher : ScholarlyEditions
ISBN 13 : 1464955808
Total Pages : 26 pages
Book Rating : 4.4/5 (649 download)

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Book Synopsis Advances in Inborn Errors Amino Acid Metabolism Research and Treatment: 2011 Edition by :

Download or read book Advances in Inborn Errors Amino Acid Metabolism Research and Treatment: 2011 Edition written by and published by ScholarlyEditions. This book was released on 2012-01-09 with total page 26 pages. Available in PDF, EPUB and Kindle. Book excerpt: Advances in Inborn Errors Amino Acid Metabolism Research and Treatment: 2011 Edition is a ScholarlyPaper™ that delivers timely, authoritative, and intensively focused information about Inborn Errors Amino Acid Metabolism in a compact format. The editors have built Advances in Inborn Errors Amino Acid Metabolism Research and Treatment: 2011 Edition on the vast information databases of ScholarlyNews.™ You can expect the information about Inborn Errors Amino Acid Metabolism in this eBook to be deeper than what you can access anywhere else, as well as consistently reliable, authoritative, informed, and relevant. The content of Advances in Inborn Errors Amino Acid Metabolism Research and Treatment: 2011 Edition has been produced by the world’s leading scientists, engineers, analysts, research institutions, and companies. All of the content is from peer-reviewed sources, and all of it is written, assembled, and edited by the editors at ScholarlyEditions™ and available exclusively from us. You now have a source you can cite with authority, confidence, and credibility. More information is available at http://www.ScholarlyEditions.com/.

Low Protein Cookery for Phenylketonuria

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Publisher : Published for the Harry A. Waisman Center on Mental Retardation and Human Development [By]
ISBN 13 :
Total Pages : 396 pages
Book Rating : 4.:/5 (89 download)

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Book Synopsis Low Protein Cookery for Phenylketonuria by : Virginia E. Schuett

Download or read book Low Protein Cookery for Phenylketonuria written by Virginia E. Schuett and published by Published for the Harry A. Waisman Center on Mental Retardation and Human Development [By]. This book was released on 1977 with total page 396 pages. Available in PDF, EPUB and Kindle. Book excerpt: Much more than a cookbook, Low Protein Cookery for PKU (Phenylketonuria) is a practical and easy-to-use guide for those who must maintain a protein-restricted diet for treatment of PKU or similar inherited diseases of protein metabolism. It contains hundreds of helpful suggestions for managing the diet. This third edition of Low Protein Cookery for PKU appears exactly twenty years alter the original 1977 publication and includes the 450-plus recipes and the hints from the 1988 second edition that have been used and enjoyed by families for nearly a decade. The major new feature of the third edition is entirely new nutrient calculations. The available food supply has changed significantly in the past fifteen years, and nutrient information is much better now. The nutrient calculations in this edition of the cookbook are based on the updated 1995 Low Protein Food List for PKU compiled by the author, which is the most widely used food list for the PKU diet in the United States. Some of the changes in nutrient values are subtle, others more significant; all reflect the best information currently available.

Krause and Mahan’s Food and the Nutrition Care Process E-Book

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Publisher : Elsevier Health Sciences
ISBN 13 : 032363656X
Total Pages : 1227 pages
Book Rating : 4.3/5 (236 download)

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Book Synopsis Krause and Mahan’s Food and the Nutrition Care Process E-Book by : Janice L Raymond

Download or read book Krause and Mahan’s Food and the Nutrition Care Process E-Book written by Janice L Raymond and published by Elsevier Health Sciences. This book was released on 2020-05-03 with total page 1227 pages. Available in PDF, EPUB and Kindle. Book excerpt: NEW! Food-Nutrient Delivery: Planning the Diet with Cultural Competency chapter provides international nutrition guidelines and resources to assist you with multicultural meal planning. NEW! Clinical: Nutritional Genomics chapter features an author from the NIH’s Human Genome Project and introduces you to the latest research about CRISPR and epigenetics. NEW! MNT for Neurologic Disorders chapter features two new authors, including a speech therapist, and displays IDDSI guidelines and an appendix for dysphagia diets to help you carefully and consistently address the nutritional needs of these patients. NEW! Clinical: Water, Electrolytes, and Acid-Base Balance and Clinical: Biochemical, Physical, and Functional Assessment chapters are updated with the most relevant and evidence-based complementary and integrative approaches to expand your expertise in these clinical nutritional areas. NEW! MNT for Adverse Reactions to Food: Food Allergies and Intolerance chapter features completely revised guidelines and a new pathophysiology algorithm to ensure you are confident in your knowledge of how to prevent emergencies and what to do when emergencies do happen. NEW! Coverage of intermittent fasting, health at every size, and health disparities focuses on the latest nutrition trends to ensure you are well-versed in these topics. NEW! The Mediterranean Diet, Choline, and Biotin appendices display at-a-glance information to help you find quickly supplemental information. NEW! Directions boxes and Focus On boxes, as well as useful websites, resources, and key terms at the end of each chapter, help you find information quickly and easily.

Maternal and Child Health Technical Information Series

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Publisher :
ISBN 13 :
Total Pages : 34 pages
Book Rating : 4.:/5 (3 download)

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Book Synopsis Maternal and Child Health Technical Information Series by :

Download or read book Maternal and Child Health Technical Information Series written by and published by . This book was released on 1986-03 with total page 34 pages. Available in PDF, EPUB and Kindle. Book excerpt:

The Practitioner's Guide to Cost-effectiveness Analysis of Nutrition Interventions

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Publisher :
ISBN 13 :
Total Pages : 70 pages
Book Rating : 4.:/5 (7 download)

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Book Synopsis The Practitioner's Guide to Cost-effectiveness Analysis of Nutrition Interventions by : Patricia L. Splett

Download or read book The Practitioner's Guide to Cost-effectiveness Analysis of Nutrition Interventions written by Patricia L. Splett and published by . This book was released on 1996 with total page 70 pages. Available in PDF, EPUB and Kindle. Book excerpt: This is a tool for learning about cost-effectiveness analysis and for developing skills in planning and carrying out evaluations that assess the cost-effectiveness of competing alternatives. The purpose of this guide is to make cost-effectiveness analysis achievable for practitioners or students interested in the nutritional well-being of clients, patients, or program participants. Designed to provide a general understanding of cost-effectiveness analysis; a step-by-step model for determining the cost-effectiveness of a nutrition intervention, program, or service; and examples of cost-effectiveness analysis applied in the field of nutrition.

Phenylketonuria

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Publisher :
ISBN 13 :
Total Pages : 1016 pages
Book Rating : 4.:/5 (31 download)

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Book Synopsis Phenylketonuria by : Edith Glicksman Neisser

Download or read book Phenylketonuria written by Edith Glicksman Neisser and published by . This book was released on 1960 with total page 1016 pages. Available in PDF, EPUB and Kindle. Book excerpt: